000 Idiopathic pleuroparenchymal fibroelastosis, PPFE

NB

IPF in the upper lobes

IDIOPATHIC PLEUROPARENCHYMAL FIBROELASTOSIS
83 year old man with COPD and emphysema presented with bilateral shoulder pain. X-ray examination of his shoulders revealed a stellate nodule in his LUL. CT showed evidence of emphysema with a 15x14mm nodule with evidence of surrounding scarring and retraction.
On PET scan the nodule was PET avid with an SUV of 4.5 consistent with a malignant neoplasm
Surgery was performed and the pathology was consistent with idiopathic pleuroparenchymal fibroelastosis
Follow up CTs 5 years following surgery have shown stability
Ashley Davidoff MD
IDIOPATHIC PLEUROPARENCHYMAL FIBROELASTOSIS
83 year old man with COPD and emphysema presented with bilateral shoulder pain. X-ray examination of his shoulders revealed a stellate nodule in his LUL. CT showed evidence of emphysema with a 15x14mm nodule with evidence of surrounding scarring and retraction.
On PET scan the nodule was PET avid with an SUV of 4.5 consistent with a malignant neoplasm
Surgery was performed and the pathology was consistent with idiopathic pleuroparenchymal fibroelastosis
Follow up CTs 5 years following surgery have shown stability
Ashley Davidoff MD
IDIOPATHIC PLEUROPARENCHYMAL FIBROELASTOSIS
83 year old man with COPD and emphysema presented with bilateral shoulder pain. X-ray examination of his shoulders revealed a stellate nodule in his LUL. CT showed evidence of emphysema with a 15x14mm nodule with evidence of surrounding scarring and retraction.
On PET scan the nodule was PET avid with an SUV of 4.5 consistent with a malignant neoplasm
Surgery was performed and the pathology was consistent with idiopathic pleuroparenchymal fibroelastosis
Follow up CTs 5 years following surgery have shown stability
Ashley Davidoff MD

 

5 YEARS POST OP

IDIOPATHIC PLEUROPARENCHYMAL FIBROELASTOSIS 5 YRS POST OP
83 year old man with COPD and emphysema presented with bilateral shoulder pain. X-ray examination of his shoulders revealed a stellate nodule in his LUL. CT showed evidence of emphysema with a 15x14mm nodule with evidence of surrounding scarring and retraction.
On PET scan the nodule was PET avid with an SUV of 4.5 consistent with a malignant neoplasm
Surgery was performed and the pathology was consistent with idiopathic pleuroparenchymal fibroelastosis
Follow up CTs 5 years following surgery have shown stability
Ashley Davidoff MD
Pleuroparenchymal fibroelastosis. Two different patients with HRCT findings suggestive of pleuroparenchymal fibroelastosis. HRCT sections, patient 1: A and B, patient 2: C and D.
Courtesy EPOS from the European Society of RadiologyReferences: RADIODIAGNÓSTICO , HOSPITAL CLÍNIC BARCELONA – Barcelona/ES
a No abnormal shadow was detected
1 year after surgical resection of the right
upper lobectomy and middle lobe partial
resection. b A subpleural and parenchymal
lesion developed in the remaining right
lung 4 years after surgical lung resection.
Respiration 2017;94:431–441

 

References and Links

Radiopaedia

 

Current Respiratory Medicine Reviews

  Case report with Spiculated nodule with PET positivity

Respirology Case Reports

Respiration – Unilateral Disease

 

INTERSTITIAL PNEUMONIA , IP