• 58 yo F
  • PMH
    • HTN, HLD, and T2DM
      • Exercise capacity remains
        • satisfactory (mMRC 2)
        • stable.
    • Imaging
      • Progressive disease
        • anterior upper lobe
        • subpleural cystic remodeling,
          • primarily in the superior segments
        • subpleural reticulations and
        • 10 years ago
          • CT
            • predominant  feature
              • lower lobe GGOs w
      • PFTs
        • moderate restriction
        • moderate/severe reduction in DLco
      • ECHO.
        • normal
    • Smoker
      • former
        • 15 PY history.
  • History
    • not suggestive of CTD
    • no clear history of familial pulmonary fibrosis.
  • ct
    • ?consistent with UIP
    • fibrotic NSIP,
    • FHP/cHP, CTD-related ILD,
    • less likely evolution of previous smoking related ILD (RB-ILD/DIP).
  • Unusual for IPF i
    • relative young age and
    • female sex
    • ? familial pulmonary fibrosis

14 years ago

 

11 years ago

Current

Cellular Infiltrate ?  mixed NSIP

ILD Discussion

? UIP vs NSIP

Presence of blood tests CD4 and cellular infiltrate favoring mixed NSIP and trial of immuno-suppression