291Lu Familial ILD

  • 58F
    • First presented 5 years  ago
      • cough and wheeze
    • Strong FH of pulmonary fibrosis
    • Lab
      • unrevealing serologies
    • PFTs
      •  restriction and
      • reduced DLCO
    • CT
      • interstitial changes on CT.
    • Bronchoscopy
      • inflammation and
      • lymphocytic predominance.
    • VATs biospy
      • fibrosis and inflammation r
      • UIP vs. Chronic hypersensitivity pneumonitis.
    • genetic testing with
      • no causative identifiable mutation
      • (MUC5B polymorphism not checked).
    • Rx
      • Nintedanib 150 mg daily for 3 years
        • stable exertional capacity
        • small fluctuations in her PFT
        • CT stable
        • Images need to be numbered
          lungs ILD Familial Indeterminate 58F

          lungs ILD Familial Indeterminate 58F b