38-year-old patient with progressive dyspnea and cough
CXR (scout for CT) shows hyperinflated lungs with increased lung volumes
CT shows bilateral and extensive thin-walled cysts surrounded by very little normal lung parenchyma.
The cysts are round and thin-walled except for air filled large irregular pocket in the right apex (image 27628/29) .
Some of the cysts do not have walls at all.
In the abdomen multiple low density lymphangioleiomyomas are present that are due to lymphatic obstruction.